Rare bleeding disorders

Overview

What is a rare bleeding disorder

There are a number of extremely rare bleeding disorders, including deficiencies of clotting Factors I, II, V, VII, X, XI, and XIII. Various recombinant and plasma-derived products are used to treat these disorders.

Factor XIII deficiency is the rarest Factor deficiency, occurring in 1 per 5 million births. It is inherited in an autosomal recessive fashion, meaning that both parents must carry the gene to pass it on to their children; it affects men and women equally.

Afibrinogenemia (a Factor I deficiency) is a rare congenital disorder characterized by absence of protein in the blood that is essential in the blood clotting (coagulation) process. This protein is known as fibrinogen or coagulation Factor I. Affected individuals may be susceptible to severe bleeding (hemorrhaging) episodes, particularly during infancy and childhood. Congenital afibrinogenemia is thought to be transmitted as an autosomal recessive trait.

Hypofibrinogenemia (a Factor I deficiency) is one of two quantitative defects, meaning the amount of fibrinogen in the blood is abnormal. Hypofibrinogenemia is when there is a low level of fibrinogen. Many people who have hypofibrinogenemia do not need treatment.

For more information, visit our website dedicated to bleeding disorders at www.hemophilia.com.


Questions regarding your rare bleeding disorder therapy

You can reach the Accredo bleeding disorder care team, anytime, day or night, seven days a week.

24-hour Customer Service Center

866-712-5200